Laparoscopıc adrenalectomy in a child wıth MEN 2A syndrome

Tander B., Abalı S., Cevık M., Hafız G.

ESPES, Vicenza, Italy, 11 - 13 September 2019, pp.156

  • Publication Type: Conference Paper / Summary Text
  • City: Vicenza
  • Country: Italy
  • Page Numbers: pp.156
  • Acibadem Mehmet Ali Aydinlar University Affiliated: Yes


We report here a case of MEN 2a syndrome and its management of diagnosis, who
treated with laparoscopic adrenalectomy.
14 years old male with neck swelling had a fine needle aspiration biopsy. The
diagnosis was medullary thyroid carcinoma. The calcitonin level was also elevated.
Hismother and grandfather had the same pathology. For the possible
pheochromacytoma, his catecholamins were found to be very high. The abdominal
MR revealed a right sided adrenal mass. A laparoscopic right adrenalectomy was
performed. The histopathologic examination revealed benign pheochromacytoma.
The diagnosis was MEN 2a syndrome and the RT c.1900T>C (p.Cys634rg) gene
mutation was found. The postoperative
alcitonin levels were dramatically decreased. He underwent total thyroidectomy and
neck dissection.The thyroid staging was T3N1M0. He is followed up for the left
adrenal gland.
In patients with MEN syndrome, the detection for pheochromacytoma has utmost
importance before any other surgery. The adrenalectomy can be performed
laparoscopically in many cases.