Paraneoplastic acrokeratosis of Bazex (Bazex's syndrome): Report of a female case associated with cholangiocarcinoma and review of the published work

Karabulut A. A., Sahin S., Sahin M., Eksioglu M., Ustun H.

JOURNAL OF DERMATOLOGY, cilt.33, sa.12, ss.850-854, 2006 (SCI-Expanded) identifier identifier identifier identifier

  • Yayın Türü: Makale / Derleme
  • Cilt numarası: 33 Sayı: 12
  • Basım Tarihi: 2006
  • Doi Numarası: 10.1111/j.1346-8138.2006.00194.x
  • Dergi Adı: JOURNAL OF DERMATOLOGY
  • Derginin Tarandığı İndeksler: Science Citation Index Expanded (SCI-EXPANDED), Scopus
  • Sayfa Sayıları: ss.850-854
  • Anahtar Kelimeler: cholangiocarcinoma, paraneoplastic acrokeratosis of Bazex, paraneoplastic dermatosis, PARA-NEOPLASTIC ACROKERATOSIS, SQUAMOUS-CELL CARCINOMA, ADENOCARCINOMA, PATIENT, WOMAN
  • Acıbadem Mehmet Ali Aydınlar Üniversitesi Adresli: Hayır

Özet

Paraneoplastic acrokeratosis of Bazex (PAB) or Bazex's syndrome is a rare, paraneoplastic syndrome that mostly affects men over 40 years old, and generally associates with squamous cell carcinoma of the upper aerodigestive tract. We describe a 57-year-old woman with the characteristic features of PAB, including violaceous erythematous, scaling eruption, palmoplantar keratoderma and nail dystrophy. Further analysis revealed the underlying neoplasm to be cholangiocarcinoma. The clinical aspects of PAB and associated neoplasms are reviewed.