Sustained hyperferritinemia in a child with macrophage activation syndrome secondary to systemic juvenile idiopathic arthritis - perforinopathy: case based review.

Cakan, Mustafa; Aktay-Ayaz, Nuray; Gemici, Hakan; Annayev, Agageldi; Citak, Agop; Akcay, Arzu; Ozturk, Gulyuz

doi:10.24953/turkjped.2018.05.022

Sustained hyperferritinemia in a child with macrophage activation syndrome secondary to systemic juvenile idiopathic arthritis - perforinopathy: case based review.

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Cakan M., Aktay-Ayaz N., Gemici H., Annayev A., Citak A. , Akcay A. , ...More

The Turkish journal of pediatrics, vol.60, no.5, pp.598-603, 2018 (Journal Indexed in SCI)

Publication Type: Article / Article
Volume: 60 Issue: 5
Publication Date: 2018
Doi Number: 10.24953/turkjped.2018.05.022
Title of Journal : The Turkish journal of pediatrics
Page Numbers: pp.598-603

Abstract

Systemic juvenile idiopathic arthritis is a subtype of juvenile idiopathic arthritis and characterized by arthritis and many systemic features like fever, rash, hepatosplenomegaly, lymphadenopathy and serositis. Macrophage activation syndrome is the most dreadful complication of systemic juvenile idiopathic arthritis and can cause mortality and morbidity if not recognized and treated early and aggressively.