Right ventricular endomyocardial fibrosis mimicking Ebstein anomaly in a patient with Behcet's disease: case report and review of the literature


Buturak A., Saygili O., Ulus S., Kalfa M., Karabulut H. , Alhan C. , et al.

MODERN RHEUMATOLOGY, cilt.24, ss.532-536, 2014 (SCI İndekslerine Giren Dergi)

  • Cilt numarası: 24 Konu: 3
  • Basım Tarihi: 2014
  • Doi Numarası: 10.3109/14397595.2013.874731
  • Dergi Adı: MODERN RHEUMATOLOGY
  • Sayfa Sayısı: ss.532-536

Özet

Behcet's disease is a multisystemic, chronic inflammatory disorder with diffuse clinical manifestations including the cardiovascular system. Endomyocardial fibrosis is a rarely seen complication of Behcet's disease leading to progressive heart failure. We report a case of right ventricular endomyocardial fibrosis mimicking Ebstein anomaly in a 26-year-old male Turkish patient with Behcet's disease, who had heart failure symptoms. In addition, the previously reported cases of endomyocardial fibrosis complicating Behcet's disease are reviewed in this article.