Right ventricular endomyocardial fibrosis mimicking Ebstein anomaly in a patient with Behcet's disease: case report and review of the literature


Buturak A., SAYGILI Ö., Ulus S., Kalfa M., Karabulut H., ALHAN C., ...Daha Fazla

MODERN RHEUMATOLOGY, cilt.24, sa.3, ss.532-536, 2014 (SCI-Expanded) identifier identifier identifier

  • Yayın Türü: Makale / Derleme
  • Cilt numarası: 24 Sayı: 3
  • Basım Tarihi: 2014
  • Doi Numarası: 10.3109/14397595.2013.874731
  • Dergi Adı: MODERN RHEUMATOLOGY
  • Derginin Tarandığı İndeksler: Science Citation Index Expanded (SCI-EXPANDED), Scopus
  • Sayfa Sayıları: ss.532-536
  • Anahtar Kelimeler: Behcet's disease, Endomyocardial fibrosis
  • Acıbadem Mehmet Ali Aydınlar Üniversitesi Adresli: Evet

Özet

Behcet's disease is a multisystemic, chronic inflammatory disorder with diffuse clinical manifestations including the cardiovascular system. Endomyocardial fibrosis is a rarely seen complication of Behcet's disease leading to progressive heart failure. We report a case of right ventricular endomyocardial fibrosis mimicking Ebstein anomaly in a 26-year-old male Turkish patient with Behcet's disease, who had heart failure symptoms. In addition, the previously reported cases of endomyocardial fibrosis complicating Behcet's disease are reviewed in this article.