Surgical treatment of Ebstein's anomaly in adult with one and a half ventricle repair: Case report

Vuran C., Omay O., Ayabakan C. , Kiliçkiran Avci B., Günaydin Ç., Yörüker U., ...More

Turkiye Klinikleri Cardiovascular Sciences, vol.23, no.3, pp.271-274, 2011 (Refereed Journals of Other Institutions) identifier

  • Publication Type: Article / Article
  • Volume: 23 Issue: 3
  • Publication Date: 2011
  • Title of Journal : Turkiye Klinikleri Cardiovascular Sciences
  • Page Numbers: pp.271-274
  • Keywords: Ebstein anomaly, Heart defects, congenital, Tricuspid valve insufficiency


Ebstein's anomaly is a rare congenital heart defect. Depends on the severity of malformations, different symptoms can be seen. Goals of surgical intervention are to increase pulmonary blood flow, to minimize tricuspid insufficiency, to reduce or eliminate right-to-left shunt, to optimize right ventricular function, and to reduce or to eliminate arrhythmias. In this article we reported surgical treatment of Ebstein's anomaly with the "one and a half ventricle repair" in two adult patients. With the use of one and a half ventricle repair; closure of the atrial septal defect resolves cyanosis, repair of tricuspid valve decreases the regurgitation from the valve and heart failure and systemic and pulmonary circulations are separated. One and a half ventricle repair can be utilized in patients with severe Ebstein's anomaly and impaired right ventricular function who are at high risk for biventricular repair. Copyright © 2011 by Türkiye Klinikleri.