Background: Glomus tumors are painful and disabling soft tissue masses arising from cutaneous arteriovenous anastomoses. They often involve the nailbed of the fingers and the toes. However, the histopathologic features are the same. Extradigital glomus tumors (EGTs) are rare lesions that involve body parts other than the hands and the feet. For this reason, initial diagnosis of extradigital glomus tumor is often late and remains a challenge for the treating phycisians because of this rare presentation and unusual localization.