Current Diagnosis and Treatment Models of Periodic Fever, Aphthous Stomatitis, Pharyngitis and Cervical Lymphadenitis Syndrome

PAÇ KISAARSLAN A., KABAKOĞLU ÜNSÜR E., SÖZERİ B.

The Journal of Pediatric Research, cilt.4, sa.2, ss.42-45, 2017 (Hakemli Dergi) identifier

  • Yayın Türü: Makale / Derleme
  • Cilt numarası: 4 Sayı: 2
  • Basım Tarihi: 2017
  • Doi Numarası: 10.4274/jpr.32757
  • Dergi Adı: The Journal of Pediatric Research
  • Derginin Tarandığı İndeksler: Other Indexes
  • Sayfa Sayıları: ss.42-45
  • Anahtar Kelimeler: Periodic fever, aphthous stomatitis, pharyngitis, and cervical lymphadenitis syndrome, diagnosis, therapy, ADENITIS PFAPA SYNDROME, ADENOPATHY SYNDROME, CHILDREN, DISORDER, PROFILE
  • Acıbadem Mehmet Ali Aydınlar Üniversitesi Adresli: Hayır

Özet

Periodic fever, aphthous stomatitis, pharyngitis, and cervical lymphadenitis (PFAPA) syndrome is the most frequent cause of periodic fever in childhood. The pathogenesis of PFAPA is still unknown. Differantial diagnosis must be made with cyclic neutropenia and other autoinflammatory diseases. Because PFAPA is self limiting and benign, there is no certain treatment model. Treatment options must be specific to the patient, with a strong family and doctor relationship.