Current Diagnosis and Treatment Models of Periodic Fever, Aphthous Stomatitis, Pharyngitis and Cervical Lymphadenitis Syndrome


PAÇ KISAARSLAN A., KABAKOĞLU ÜNSÜR E., SÖZERİ B.

The Journal of Pediatric Research, vol.4, no.2, pp.42-45, 2017 (Peer-Reviewed Journal) identifier

  • Publication Type: Article / Review
  • Volume: 4 Issue: 2
  • Publication Date: 2017
  • Doi Number: 10.4274/jpr.32757
  • Journal Name: The Journal of Pediatric Research
  • Journal Indexes: Other Indexes
  • Page Numbers: pp.42-45
  • Keywords: Periodic fever, aphthous stomatitis, pharyngitis, and cervical lymphadenitis syndrome, diagnosis, therapy, ADENITIS PFAPA SYNDROME, ADENOPATHY SYNDROME, CHILDREN, DISORDER, PROFILE
  • Acibadem Mehmet Ali Aydinlar University Affiliated: Yes

Abstract

Periodic fever, aphthous stomatitis, pharyngitis, and cervical lymphadenitis (PFAPA) syndrome is the most frequent cause of periodic fever in childhood. The pathogenesis of PFAPA is still unknown. Differantial diagnosis must be made with cyclic neutropenia and other autoinflammatory diseases. Because PFAPA is self limiting and benign, there is no certain treatment model. Treatment options must be specific to the patient, with a strong family and doctor relationship.