Topsy-Turvy Heart: A Very Rare Congenital Rotational Heart Disease With Tracheobronchial Anomalies


Erek E., Guzeltas A., Ozturk N. Y. , KIYAN G., Karakoc F., AKALIN F., ...More

WORLD JOURNAL FOR PEDIATRIC AND CONGENITAL HEART SURGERY, vol.4, no.3, pp.308-311, 2013 (Journal Indexed in ESCI) identifier identifier identifier

  • Publication Type: Article / Article
  • Volume: 4 Issue: 3
  • Publication Date: 2013
  • Doi Number: 10.1177/2150135113476718
  • Title of Journal : WORLD JOURNAL FOR PEDIATRIC AND CONGENITAL HEART SURGERY
  • Page Numbers: pp.308-311

Abstract

The topsy-turvy heart is characterized by a global 90 degrees clockwise rotation around the heart's long axis. This rotation displaces all basal great arteries inferiorly and posteriorly, resulting in elongation and stretching of the brachiocephalic arteries and the bronchi. To date, reports of only four living cases have been published in the literature. We report here three new cases, with additional aortopulmonary window defects, and present their morphological details, clinical presentations, and our management.