Cardiac pathologies and clinical follow-up of patients with Williams syndrome

Sarisoy, Ozlem; Ayabakan, CANAN; Tokel, Kursad; Saritas, Bulent; Vuran, Can; Ozker, Emre; Turkoz, Rasa

doi:10.5606/tgkdc.dergisi.2013.7404

Cardiac pathologies and clinical follow-up of patients with Williams syndrome

Sarisoy O., Ayabakan C., Tokel K., Saritas B., Vuran C., Ozker E., ...Daha Fazla

TURK GOGUS KALP DAMAR CERRAHISI DERGISI-TURKISH JOURNAL OF THORACIC AND CARDIOVASCULAR SURGERY, cilt.21, sa.4, ss.1027-1031, 2013 (SCI-Expanded)

Yayın Türü: Makale / Tam Makale
Cilt numarası: 21 Sayı: 4
Basım Tarihi: 2013
Doi Numarası: 10.5606/tgkdc.dergisi.2013.7404
Dergi Adı: TURK GOGUS KALP DAMAR CERRAHISI DERGISI-TURKISH JOURNAL OF THORACIC AND CARDIOVASCULAR SURGERY
Derginin Tarandığı İndeksler: Science Citation Index Expanded (SCI-EXPANDED), Scopus, TR DİZİN (ULAKBİM)
Sayfa Sayıları: ss.1027-1031
Anahtar Kelimeler: Aortic stenosis, clinical follow-up, pulmonary stenosis, Williams syndrome, SUPRAVALVULAR AORTIC-STENOSIS, BEUREN-SYNDROME, PULMONARY, OUTCOMES, CHILDREN
Acıbadem Mehmet Ali Aydınlar Üniversitesi Adresli: Hayır

Özet

Between August 2008 and August 2011, nine patients (3 girls, 6 boys; mean age 19 +/- 29 months) were admitted to our clinic with Williams syndrome. The mean body weight of the patients was 9454 +/- 5880 g. Two patients had supravalvular aortic stenosis (sAS), one had periferal pulmonary stenosis (PPS), one had supravalvular PS (sPS), two had sAS and sPS, and three had sAS and bilateral PPS. Two patients were not operated. Four patients were operated for sAS and PPS, one patient for sAS, valvular and sPS, one patient for PPS and sPS, and one patient for sAS operation. The gradients were decreased and remained unchanged during follow-up.