Malignant nerve sheath tumor of oculomotor nerve in a pediatric patient

Altinbas E., TANRIKULU B., ERŞEN DANYELİ A., ÖZEK Ö. M. M.

CHILDS NERVOUS SYSTEM, vol.38, no.4, pp.807-811, 2022 (SCI-Expanded) identifier identifier identifier

  • Publication Type: Article / Article
  • Volume: 38 Issue: 4
  • Publication Date: 2022
  • Doi Number: 10.1007/s00381-021-05283-9
  • Journal Name: CHILDS NERVOUS SYSTEM
  • Journal Indexes: Science Citation Index Expanded (SCI-EXPANDED)
  • Page Numbers: pp.807-811
  • Keywords: Malignant nerve sheath tumor, Oculomotor nerve, Pediatric age
  • Acibadem Mehmet Ali Aydinlar University Affiliated: Yes

Abstract

Malignant nerve sheath tumors are extremely rare pathologies. They tend to occur within peripheral nerves and have close association of neurofibromatosis disease. Here, we present the second case of MNST of oculomotor nerve in literature. The patient was a 2-year-old girl with left sided oculomotor nerve palsy. After resection, the patient immediately had chemotherapy and radiotherapy. One year after surgery disease progressed with extensive intracranial seedings, and she passed away.