Malignant nerve sheath tumor of oculomotor nerve in a pediatric patient


Altinbas E., TANRIKULU B. , ERŞEN DANYELİ A. , ÖZEK Ö. M. M.

CHILDS NERVOUS SYSTEM, 2021 (Journal Indexed in SCI) identifier identifier identifier

  • Publication Type: Article / Article
  • Volume:
  • Publication Date: 2021
  • Doi Number: 10.1007/s00381-021-05283-9
  • Title of Journal : CHILDS NERVOUS SYSTEM
  • Keywords: Malignant nerve sheath tumor, Oculomotor nerve, Pediatric age

Abstract

Malignant nerve sheath tumors are extremely rare pathologies. They tend to occur within peripheral nerves and have close association of neurofibromatosis disease. Here, we present the second case of MNST of oculomotor nerve in literature. The patient was a 2-year-old girl with left sided oculomotor nerve palsy. After resection, the patient immediately had chemotherapy and radiotherapy. One year after surgery disease progressed with extensive intracranial seedings, and she passed away.