Univentricular heart and Cantrell syndrome in a pediatric case
TURK GOGUS KALP DAMAR CERRAHISI DERGISI-TURKISH JOURNAL OF THORACIC AND CARDIOVASCULAR SURGERY, cilt.24, sa.3, ss.542-544, 2016 (SCI-Expanded, Scopus, TRDizin)
- Yayın Türü: Makale / Tam Makale
- Cilt numarası: 24 Sayı: 3
- Basım Tarihi: 2016
- Doi Numarası: 10.5606/tgkdc.dergisi.2016.12090
- Dergi Adı: TURK GOGUS KALP DAMAR CERRAHISI DERGISI-TURKISH JOURNAL OF THORACIC AND CARDIOVASCULAR SURGERY
- Derginin Tarandığı İndeksler: Science Citation Index Expanded (SCI-EXPANDED), Scopus, TR DİZİN (ULAKBİM)
- Sayfa Sayıları: ss.542-544
- Anahtar Kelimeler: Cantrell syndrome, single ventricle, ventricular diverticulum, PENTALOGY
- Acıbadem Mehmet Ali Aydınlar Üniversitesi Adresli: Evet
Özet
Cantrell syndrome is a rare syndrome associated with varying degrees of midline wall defects and congenital cardiac anomalies. In this article, we report a six-year-old girl with Cantrell syndrome associated with single ventricle, pulmonary stenosis, ventricular diverticulum, bilateral superior vena cava, lower sternal, and supra-umbilical abdominal anterior wall defect. The patient, who had no previous intervention despite severe cyanosis (SpO(2): 65 to 70%) due to the parent decision, underwent operation. Bilateral Glenn procedure, resection of the ventricular diverticulum, and anterior abdominal wall repair were performed in collaboration with pediatric surgery. The patient was discharged uneventfully with a SpO(2) of 80 to 85%. No problem was observed in the postoperative sixth month visit.