Univentricular heart and Cantrell syndrome in a pediatric case
TURK GOGUS KALP DAMAR CERRAHISI DERGISI-TURKISH JOURNAL OF THORACIC AND CARDIOVASCULAR SURGERY, vol.24, no.3, pp.542-544, 2016 (SCI-Expanded, Scopus, TRDizin)
- Publication Type: Article / Article
- Volume: 24 Issue: 3
- Publication Date: 2016
- Doi Number: 10.5606/tgkdc.dergisi.2016.12090
- Journal Name: TURK GOGUS KALP DAMAR CERRAHISI DERGISI-TURKISH JOURNAL OF THORACIC AND CARDIOVASCULAR SURGERY
- Journal Indexes: Science Citation Index Expanded (SCI-EXPANDED), Scopus, TR DİZİN (ULAKBİM)
- Page Numbers: pp.542-544
- Keywords: Cantrell syndrome, single ventricle, ventricular diverticulum, PENTALOGY
- Acibadem Mehmet Ali Aydinlar University Affiliated: Yes
Abstract
Cantrell syndrome is a rare syndrome associated with varying degrees of midline wall defects and congenital cardiac anomalies. In this article, we report a six-year-old girl with Cantrell syndrome associated with single ventricle, pulmonary stenosis, ventricular diverticulum, bilateral superior vena cava, lower sternal, and supra-umbilical abdominal anterior wall defect. The patient, who had no previous intervention despite severe cyanosis (SpO(2): 65 to 70%) due to the parent decision, underwent operation. Bilateral Glenn procedure, resection of the ventricular diverticulum, and anterior abdominal wall repair were performed in collaboration with pediatric surgery. The patient was discharged uneventfully with a SpO(2) of 80 to 85%. No problem was observed in the postoperative sixth month visit.