Bilateral adrenal cystic neuroblastoma with superior vena cava syndrome and massive intracystic haemorrhage

Pinarli F., Danaci M., TANDER B. , Dagdemir A., Diren B., Acar S., ...More

PEDIATRIC RADIOLOGY, vol.34, no.9, pp.746-749, 2004 (Journal Indexed in SCI) identifier identifier identifier identifier

  • Publication Type: Article / Article
  • Volume: 34 Issue: 9
  • Publication Date: 2004
  • Doi Number: 10.1007/s00247-004-1209-5
  • Title of Journal : PEDIATRIC RADIOLOGY
  • Page Numbers: pp.746-749
  • Keywords: adrenal neuroblastoma, cyst, haemorrhage, superior vena cava syndrome, ultrasound, CT, child, NEURO-BLASTOMA, FEATURES, HEMOPERITONEUM, CHILDHOOD


Bilateral cystic adrenal tumours are a rare presentation of neuroblastoma. Intratumoural haemorrhage is a frequent finding in neuroblastoma, but is rarely symptomatic. We present an 11-month-old girl with predominantly cystic bilateral neuroblastomas and distant lymph-node metastasis. Massive intracystic haemorrhage and superior vena cava (SVC) syndrome were ominous prognostic factors, leading to death. Large tumours with intracystic haemorrhage might require a conservative approach.