Successful repair of infantile scimitar syndrome with contralateral pulmonary vein stenosis in an infant


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Onalan M. A. , TEMUR B. , AYDIN S. , EREK E.

Brazilian Journal of Cardiovascular Surgery, vol.36, no.1, pp.133-136, 2021 (Journal Indexed in SCI) identifier identifier identifier

  • Publication Type: Article / Article
  • Volume: 36 Issue: 1
  • Publication Date: 2021
  • Doi Number: 10.21470/1678-9741-2019-0228
  • Title of Journal : Brazilian Journal of Cardiovascular Surgery
  • Page Numbers: pp.133-136
  • Keywords: Pulmonary Syndrome, Pulmonary Veins, Respiratory System Abnormalities, Heart Defects, Congenital, Survivors, OUTCOMES

Abstract

© 2021, Sociedade Brasileira de Cirurgia Cardiovascular. All rights reserved.Infantile scimitar syndrome (SS) is a rare congenital heart disease and has high mortality. Guidelines have not been established, but surgery is indicated in symptomatic patients. Despite the various surgical approaches, outcomes continue to be disappointing. We present our surgical experience with an infantile SS patient who had stenotic pulmonary veins contralateral to the hypoplastic lung with complicated anatomy. There are few cases with this complex pathology in the literature. Moreover, our patient was the first transplant-free survivor with this complexity in the literature.